ABSTRACT
Os autores apresentam o emprego de cuma endoprótese convencional de metade proxímal do fêmur com o componente acetabular bloqueado em um paciente com condrossarcoma secundário à doença de Ollier; discutem sua indicaçäo, resultado funcional imediato e a evoluçäo do caso
Subject(s)
Humans , Male , Adult , Chondrosarcoma/secondary , Enchondromatosis/pathology , Femoral Neoplasms/secondary , Joint Prosthesis , Bone Neoplasms/secondary , Bone Neoplasms , Chondrosarcoma/surgery , Femoral Neoplasms/surgeryABSTRACT
This is a 37 years old female with diagnosis of osteochondromatosis of the fibula: six months afterwardas develops left iliopubic destruction. The pathology reports chondrosarcoma, a hemipelvectomy is performed preserving the limb. No complications were present in the post- operative period; she started partial weigh bearing with cruches three months after surgery. Commentaries about primary and secundary chondrosarcoma are mode
Subject(s)
Humans , Female , Adult , Middle Aged , Chondrosarcoma/surgery , Hemipelvectomy , Ileal Neoplasms/surgery , Chondrosarcoma/secondary , Ileal Neoplasms/secondary , Osteochondromatosis/pathologyABSTRACT
Os autores relatam um caso de retinoblastoma familiar associado ao aparecimento de um segundo tumor primário näo ocular e discutem possíveis teorias genéticas que predisporiam a estas duas neoplasias
Subject(s)
Adult , Humans , Male , Chondrosarcoma/secondary , Eye Neoplasms/genetics , Maxillary Neoplasms/secondary , Retinoblastoma/genetics , Chondrosarcoma/diagnosis , Chondrosarcoma/therapy , Eye Neoplasms/diagnosis , Eye Neoplasms/therapy , Maxillary Neoplasms/diagnosis , Maxillary Neoplasms/therapy , Retinoblastoma/diagnosis , Retinoblastoma/therapyABSTRACT
Os autores relatam um caso operado no Hospital Naval Marcílio Dias. Pacietne potador de condrosarcoma foi submetido a ressecçäo segmentar do fêmur com substituiçäo por endoprótese näo convencional. A execuçäo deste procedimento impede que se mutile o paciente permitindo a preservaçäo da funçäo do membro doente